Unusual coarctation-the PHACE syndrome: report of three cases.

Abstract

OBJECTIVES: To report the clinical features, nature of vasculopathy observed and the management instituted in three cases of PHACE syndrome.RESULTS: All three patients were noted to have diffuse vasculopathy and aortic arch hypoplasia in addition to aortic coarctation adding substantial surgical risk or making surgery palliative.CONCLUSION: PHACE syndrome should be considered in the differential diagnosis of aortic coarctation associated with aortic arch hypoplasia.